Aka
monosuperocentroincisivodontic dwarfism.
Presentation
Midline symmetrical upper central incisor.
The condition may also be associated with other midline disturbances such as
cleft palate
choanal stenosis or atresia
imperforate anus, or
umbilical hernia.
It is part of the spectrum of the holoprosencephaly malformation complex.
Of importance is the association with hypoplasia of the sella, pituitary dysfunction, growth hormone deficiency and subsequent short stature.
Adapted from "Handbook of Pediatric Dentistry" Editors: Cameron, Widmar. Mosby - Wolfe.